familial ossifying fibroma

Gigantiform cementoma

Gigantiform cementoma is a rare, autosomal dental tumor. The tumor is benign, but without intervention can result in severe disfigurement of the jaw and facial skeleton. It is commonly found in the mandible and the maxilla but it is less commonly found in the maxilla. The tumor can be found between the premolars and the molars. The cause of this tumor is currently unknown although recent research suggests a relationship between gigantiform cementoma and Gnathodiaphyseal dysplasia (GDD). The tumor is considered rare with only a few documented cases worldwide. The most famous case is of Novemthree Siahaan (who died on September 15, 2005), an Indonesian boy from Batam Island who received medical care in Haulien, Taiwan through a Buddhist missionary from the Tzu Chi Foundation, which was documented on the Discovery Health Channel. Another famous case involves a Korean girl named Ayun Lee (August 26, 2003~) and her father Young-hak Lee which suggests that the tumor may be heritable. Lee is currently under treatment. The tumor is most prevalent in females averaging 42 years old. The condition typically affects adults between the ages of 20 and 50, with higher incidence in women than men. There is a chance to get passed down but in recent research it is said that most cases are sporadic and not inherited. The term has been used in the past to describe florid cemento-osseous dysplasia, but it is now reserved for an autosomal dominant condition affecting the maxillae. There is still not enough research to confirm whether it predominantly affects on specific group but it is a rare...